| Identification |
| HMDB Protein ID
| CDBP02218 |
| Secondary Accession Numbers
| Not Available |
| Name
| Glycine cleavage system H protein, mitochondrial |
| Description
| Not Available |
| Synonyms
|
Not Available
|
| Gene Name
| GCSH |
| Protein Type
| Enzyme |
| Biological Properties |
| General Function
| Involved in glycine catabolic process |
| Specific Function
| The glycine cleavage system catalyzes the degradation of glycine. The H protein shuttles the methylamine group of glycine from the P protein to the T protein.
|
| GO Classification
|
| Biological Process |
| glycine catabolic process |
| glycine decarboxylation via glycine cleavage system |
| Cellular Component |
| mitochondrion |
| glycine cleavage complex |
| Component |
| mitochondrion |
| macromolecular complex |
| protein complex |
| organelle |
| membrane-bounded organelle |
| intracellular membrane-bounded organelle |
| glycine cleavage complex |
| Molecular Function |
| aminomethyltransferase activity |
| Process |
| glycine metabolic process |
| glycine catabolic process |
| cellular amino acid and derivative metabolic process |
| cellular amino acid metabolic process |
| metabolic process |
| cellular metabolic process |
| glycine decarboxylation via glycine cleavage system |
| serine family amino acid metabolic process |
|
| Cellular Location
|
- Mitochondrion
|
| Pathways
|
| Name | SMPDB/Pathwhiz | KEGG | | Glyoxylate and dicarboxylate metabolism | Not Available |  | | Ammonia Recycling |    |  |
|
| Gene Properties |
| Chromosome Location
| Not Available |
| Locus
| Not Available |
| SNPs
| GCSH |
| Gene Sequence
|
>522 bp
ATGGCGCTGCGAGTGGTGCGGAGCGTGCGGGCCCTGCTCTGCACCCTGCGCGCGGTCCCG
TTACCCGCCGCGCCCTGCCCGCCGAGGCCCTGGCAGCTGGGGGTGGGCGCCGTCCGTACG
CTGCGCACTGGACCCGCTCTGCTCTCGGTGCGTAAATTCACAGAGAAACACGAATGGGTA
ACAACAGAAAATGGCATTGGAACAGTGGGAATCAGCAATTTTGCACAGGAAGCGTTGGGA
GATGTTGTTTATTGTAGTCTCCCTGAAGTTGGGACAAAATTGAACAAACAAGATGAGTTT
GGTGCTTTGGAAAGTGTGAAAGCTGCTAGTGAACTCTATTCTCCTTTATCAGGAGAAGTA
ACTGAAATTAATGAAGCTCTTGCAGAAAATCCAGGACTTGTAAACAAATCTTGTTATGAA
GATGGTTGGCTGATCAAGATGACACTGAGTAACCCTTCAGAACTAGATGAACTTATGAGT
GAAGAAGCATATGAGAAATACATAAAATCTATTGAGGAGTGA
|
| Protein Properties |
| Number of Residues
| 173 |
| Molecular Weight
| Not Available |
| Theoretical pI
| Not Available |
| Pfam Domain Function
|
|
| Signals
|
Not Available
|
|
Transmembrane Regions
|
Not Available
|
| Protein Sequence
|
>Glycine cleavage system H protein, mitochondrial
MALRVVRSVRALLCTLRAVPLPAAPCPPRPWQLGVGAVRTLRTGPALLSVRKFTEKHEWV
TTENGIGTVGISNFAQEALGDVVYCSLPEVGTKLNKQDEFGALESVKAASELYSPLSGEV
TEINEALAENPGLVNKSCYEDGWLIKMTLSNPSELDELMSEEAYEKYIKSIEE
|
| External Links |
| GenBank ID Protein
| Not Available |
| UniProtKB/Swiss-Prot ID
| P23434 |
| UniProtKB/Swiss-Prot Entry Name
| GCSH_HUMAN |
| PDB IDs
|
Not Available |
| GenBank Gene ID
| M69175 |
| GeneCard ID
| GCSH |
| GenAtlas ID
| GCSH |
| HGNC ID
| HGNC:4208 |
| References |
| General References
| Not Available |