| Identification |
| HMDB Protein ID
| CDBP00122 |
| Secondary Accession Numbers
| Not Available |
| Name
| NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 1 |
| Description
| Not Available |
| Synonyms
|
- CI-MWFE
- Complex I-MWFE
- NADH-ubiquinone oxidoreductase MWFE subunit
|
| Gene Name
| NDUFA1 |
| Protein Type
| Enzyme |
| Biological Properties |
| General Function
| Involved in NADH dehydrogenase (ubiquinone) activity |
| Specific Function
| Accessory subunit of the mitochondrial membrane respiratory chain NADH dehydrogenase (Complex I), that is believed not to be involved in catalysis. Complex I functions in the transfer of electrons from NADH to the respiratory chain. The immediate electron acceptor for the enzyme is believed to be ubiquinone |
| GO Classification
|
Not Available
|
| Cellular Location
|
- Single-pass membrane protein
- Mitochondrion inner membrane
- Matrix side
|
| Pathways
|
| Name | SMPDB/Pathwhiz | KEGG | | Mitochondrial Electron Transport Chain |    |  |
|
| Gene Properties |
| Chromosome Location
| Not Available |
| Locus
| Not Available |
| SNPs
| NDUFA1 |
| Gene Sequence
|
>213 bp
ATGTGGTTCGAGATTCTCCCCGGACTCTCCGTCATGGGCGTGTGCTTGTTGATTCCAGGA
CTGGCTACTGCGTACATCCACAGGTTCACTAACGGGGGCAAGGAAAAAAGGGTTGCTCAT
TTTGGGTATCACTGGAGTCTGATGGAAAGAGATAGGCGCATCTCTGGAGTTGATCGTTAC
TATGTGTCAAAGGGTTTGGAGAACATTGATTAA
|
| Protein Properties |
| Number of Residues
| 70 |
| Molecular Weight
| 8072.3 |
| Theoretical pI
| 9.12 |
| Pfam Domain Function
|
Not Available |
| Signals
|
|
|
Transmembrane Regions
|
|
| Protein Sequence
|
>NADH dehydrogenase [ubiquinone] 1 alpha subcomplex subunit 1
MWFEILPGLSVMGVCLLIPGLATAYIHRFTNGGKEKRVAHFGYHWSLMERDRRISGVDRY
YVSKGLENID
|
| External Links |
| GenBank ID Protein
| 12653011 |
| UniProtKB/Swiss-Prot ID
| O15239 |
| UniProtKB/Swiss-Prot Entry Name
| NDUA1_HUMAN |
| PDB IDs
|
Not Available |
| GenBank Gene ID
| BC000266 |
| GeneCard ID
| NDUFA1 |
| GenAtlas ID
| NDUFA1 |
| HGNC ID
| HGNC:7683 |
| References |
| General References
| Not Available |